Research Activities

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Based on the data in the PROGNOSIS registry, it is planned to establish further basic research-oriented and translational projects.

Through intensive research activities, the subject of NCFB should also increasingly play a role at German congresses.

Professor Dr. Tobias Welte and Dr. Felix Ringshausen, both from Hannover Medical School, are the German representatives participating in the ERS Task Force to develop a European guideline: the ERS Clinical Practice Guideline for the Management of Bronchiectasis.

The translation and commentary for the German language trinational (AT-CH-DE) guideline is being planned.

Publications in German language

Management der Primären Ciliären Dyskinesie

Raidt, J., Brillault, J., Brinkmann, F., Jung, A., Koerner-Rettberg, C., Koitschev, A., Linz-Keul, H., Nüßlein, T., Ringshausen, F. C., Röhmel, J., Rosewich, M., Werner, C. and Omran, H.

Pneumologie (Nov 2020)

Risikoabschätzung bei Patienten mit chronischen Atemwegs- und Lungenerkrankungen im Rahmen der SARS-CoV-2-Pandemie

Lommatzsch, M., Rabe, K. F., Taube, C., Joest, M., Kreuter, M., Wirtz, H., Blum, T. G., Kolditz, M., Geerdes-Fenge, H., Otto-Knapp, R., Häcker, B., Schaberg, T., Ringshausen, F. C., Vogelmeier, C. F., Reinmuth, N., Reck, M., Gottlieb, J., Konstantinides, S., Meyer, F. J., Worth, H., Windisch, W., Welte, T. and Bauer, T.

Pneumologie (Nov 26 2020)

S3-Leitlinie: Lungenerkrankung bei Mukoviszidose – Modul 2: Diagnostik und Therapie bei der chronischen Infektion mit Pseudomonas aeruginosa

Schwarz, C., Schulte-Hubbert, B., Bend, J., Abele-Horn, M., Baumann, I., Bremer, W., Brunsmann, F., Dieninghoff, D., Eickmeier, O., Ellemunter, H., Fischer, R., Grosse-Onnebrink, J., Hammermann, J., Hebestreit, H., Hogardt, M., Hugel, C., Hug, M., Illing, S., Jung, A., Kahl, B., Koitschev, A., Mahlberg, R., Mainz, J. G., Mattner, F., Mehl, A., Moller, A., Muche-Borowski, C., Nusslein, T., Puderbach, M., Renner, S., Rietschel, E., Ringshausen, F. C., Schmidt, S., Sedlacek, L., Sitter, H., Smaczny, C., Tummler, B., Vonberg, R., Wielputz, M. O., Wilkens, H., Wollschlager, B., Zerlik, J., Duesberg, U. and van Koningsbruggen-Rietschel, S.

Pneumologie (May 2018)

Messung des nasalen Stickstoffmonoxids und ein modifizierter PICADAR-Score als Screening für primär ciliäre Dyskinesie in Erwachsenen mit Bronchiektasen

Rademacher, J., Buck, A., Schwerk, N., Price, M., Fuge, J., Welte, T. and Ringshausen, F. C.

Pneumologie (Aug 2017)

Lungenerkrankung durch nichttuberkulöse Mykobakterien

Ringshausen FC, Rademacher J.

Internist (Berl). 2016;57(2):142-52

Aktuelle Ăśbersicht Bonchiektasen

Rademacher J, Ringshausen FC.

COPD in Deutschland. 2015 Aug; 50-52

PROGNOSIS – The PROspective German NOn-CF BronchiectaSIS Patient Registry

Rademacher J, de Roux A, Ringshausen FC.

Pneumologie. 2015 Jul;69(7):391-3

Therapie von Bronchiektasen

Rademacher J, Schweigert M.

Zentralbl Chir. 2015 Feb;140(1):113-26; quiz 127-8

Nicht durch eine zystische Fibrose bedingte (Non-CF-) Bronchiektasen

Ringshausen FC, Rademacher J, Welte T.

Dtsch Med Wochenschr. 2014 Apr;139(14):707-10

Non-CF-Bronchiektasen mit Fokus auf die allergische bronchopulmonale Aspergillose

Rademacher J, Ringshausen FC.

Pneumologie. 2013 Jan; 67(1):40-7; 48-9

Bronchiektasen – Diagnostik und Therapie

Rademacher J, Welte T.

Dtsch Arztebl Int. 2011 Dec;108(48):809-15

EinfĂĽhrung zum Thema Bronchiektasen

Ringshausen FC, Welte T.

Der Pneumologe. 2014/4

Leitthema Epidemiologie von Non-CF-Bronchiektasen

Rademacher J, Ringshausen FC.

Pneumologe. 2014/4

Leitthema Diagnostik von Bronchiektasen

Dr. N. Derichs.

Pneumologe. 2014/4

Leitthema Atemtherapie bei Non-CF-Bronchiektasen

BrĂĽckner U.

Pneumologe. 2014/4

Leitthema Pneumologische Rehabilitation bei Non CF-Bronchiektasen

Glöckl R, Kenn K.

Pneumologe. 2014/4

Leitthema Inhalative Antibiotikatherapie bei Non-CF-Bronchiektasen

Flick H, Meilinger M, Wagner M, Olschewski H, Eber E.

Pneumologe. 2014/4

Leitthema Versorgung von Patienten mit Non-CF-Bronchiektasen in der niedergelassenen Praxis

de Roux A.

Pneumologe. 2014/4

Current Studies

Up to now, only a few controlled studies have been performed, so that hardly any evidence-based recommendations could be submitted for non-CF bronchiectasis.

At the present time, the efficacy of many different substances is being tested. A hypertonic saline solution is often used clinically as it has been shown to be effective in CF, although this has not yet been documented for non-CF bronchiectasis.

After good results in the Phase II studies, inhalational mannitol is now in Phase III clinical trials.

Inhalational antibiotics could be of importance, particularly in patients populated with gram-negative bacteria. Tobramycin and colistin are well established – though not registered – aztreonam, ciprofloxacin and gentamicin are being tested in clinical studies. Macrolides, however, according to the results of several studies with only small sample size, seem to have an additional effect. Long-term therapy with inhalational antibiotics and/or macrolides is only indicated if a clearly positive effect (decreased amount of sputum, no exacerbation) is achieved within three months from start of therapy.

ERADICATE-STUDIE

For Doctors

Taking care of frequently exacerbating patients

An interview with Dr. Felix C. Ringshausen and Prof. Dr. Tobias Welte (in German)